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Nature Reviews Rheumatology (2024). [2] ANCA-associated vasculitis. Nature Reviews Disease Primers (2020). [3] Diagnosis and management of ANCA-associated vasculitis. The Lancet (2024).
Anti-C1q antibodies were detected among 74.3% of patients, with levels significantly higher among those with active vs inactive disease (median, 19.9 vs 13.3 U/mL; P =.03).
VEXAS syndrome is known to be a mimicker of ANCA-associated vasculitis, making it a challenge to distinguish between the disorders. VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic ...
TOPLINE: Rituximab and cyclophosphamide are equally effective in achieving remission or low disease activity rates in childhood-onset antineutrophil cytoplasmic antibody–associated vasculitis ...
Antineutrophil cytoplasmic antibody-associated vasculitis (AAV) is a severe autoimmune condition in which circulating autoantibodies target components of neutrophils, notably proteinase 3 and ...